Essential Biochemistry - Protein Metabolism (Section 2 - No. 7)
Which enzyme deficiency is associated with tyrosinemia type I?
Fumarylacetoacetate hydrolase
Tyrosinase
Homogentisate dioxygenase
Phenylalanine hydroxylase
Explanation
Tyrosinemia type I is due to a deficiency of fumarylacetoacetate hydrolase.
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