Essential Biochemistry - Lipid Metabolism (Section 10 - No. 46)

Which enzyme is deficient in Tay-Sachs disease?
Hexosaminidase A
β-galactosidase
Sphingomyelinase
Glucocerebrosidase

Explanation

Tay-Sachs disease is caused by a deficiency of Hexosaminidase A.

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