Essential Biochemistry - Hemoglobin Metabolism (Section 3 - No. 7)
Which enzyme is deficient in congenital erythropoietic porphyria?
Uroporphyrinogen I synthase
Uroporphyrinogen III synthase
Uroporphyrinogen decarboxylase
Ferrochelatase
Explanation
Uroporphyrinogen III synthase is deficient in congenital erythropoietic porphyria.
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