Essential Biochemistry - Hemoglobin Metabolism (Section 3 - No. 33)
Which enzyme is deficient in acute intermittent porphyria?
Uroporphyrinogen I synthase
Aminolevulinate dehydratase
Uroporphyrinogen III synthase
Ferrochelatase
Explanation
Uroporphyrinogen I synthase is deficient in acute intermittent porphyria.
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