Essential Biochemistry - Hemoglobin Metabolism (Section 2 - No. 6)
Which enzyme deficiency causes hepatic porphyria?
Uroporphyrinogen I synthase
Coproporphyrinogen oxidase
Uroporphyrinogen decarboxylase
Ferrochelatase
Explanation
Uroporphyrinogen decarboxylase deficiency is the cause of hepatic porphyria.
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