Essential Biochemistry - Hemoglobin Metabolism (Section 2 - No. 37)

Which enzyme is defective in Crigler-Najjar syndrome?
Heme oxygenase
UDP-glucuronosyltransferase
ALA synthase
Ferrochelatase

Explanation

UDP-glucuronosyltransferase is defective in Crigler-Najjar syndrome.

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