Essential Biochemistry - Hemoglobin Metabolism (Section 2 - No. 3)
What enzyme is deficient in acute intermittent porphyria?
ALA synthase
ALA dehydratase
Porphobilinogen deaminase
Uroporphyrinogen decarboxylase
Explanation
Porphobilinogen deaminase is deficient in acute intermittent porphyria.
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