Essential Biochemistry - Hemoglobin Metabolism (Section 2 - No. 12)

Which enzyme is deficient in acute intermittent porphyria?
ALA synthase
ALA dehydratase
Porphobilinogen deaminase
Uroporphyrinogen decarboxylase

Explanation

Porphobilinogen deaminase is deficient in acute intermittent porphyria.

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